Epidermolysis bullosa (EB) encompasses a collection of skin conditions characterized by blister formation. This condition renders the skin extremely delicate, making it susceptible to blistering even with minor friction. In some instances, individuals with EB may not perceive the rubbing or injury that leads to blister formation.
In severe instances, blisters extend beyond the surface of the skin and can develop internally, affecting areas such as the linings of the mouth, esophagus, stomach, intestines, upper airway, bladder, and genital region.
Treatment and Care
Individuals with mild cases of Epidermolysis Bullosa (EB) may not necessitate extensive treatment. However, they should focus on preventing blister formation and minimizing infection risk when blisters do occur. For those with moderate to severe manifestations, managing the condition involves addressing various complications and may require psychological support alongside meticulous skin and tissue care and protection.
When blisters develop, the primary goals of care include alleviating pain or discomfort, preventing excessive fluid loss, facilitating healing, and averting infections. Medical practitioners may recommend mild analgesics to mitigate discomfort during dressing changes. Dressings adhering to the skin can be gently removed by soaking them in warm water.
While daily cleansing may involve bathing with mild soaps, it may be more manageable to bathe in sections, cleaning small areas at a time. In cases where blisters enlarge and may result in significant wounds upon rupture, healthcare professionals will provide guidance on safely addressing blisters in their early stages while preserving the integrity of the overlying skin.